JOURNAL OF THE CZECH PEDIATRIC SOCIETY AND THE SLOVAK PEDIATRIC SOCIETY

Čes-slov Pediat 2025, 80(3):148-153 | DOI: 10.55095/CSPediatrie2025/019

Current management options of Pierre-Robin sequence

Vojtěch Novotný1, Magdalena Koťová2, 3, Tereza Doušová1, Barbora Obermannová1
1 Pediatrická klinika, 2. lékařská fakulta, Univerzita Karlova a Fakultní nemocnice v Motole, Praha
2 Stomatologická klinika, 2. lékařská fakulta, Univerzita Karlova a Fakultní nemocnice Královské Vinohrady, Praha
3 Rozštěpové centrum Praha, Fakultní nemocnice Královské Vinohrady, Praha

Pierre Robin Sequence (PRS) is a congenital condition characterized by micrognathia, glossoptosis, and, in some patients, cleft palate of varying extent. This leads to upper airway obstruction and feeding difficulties. PRS requires a comprehensive approach that combines multidisciplinary care with both surgical and non-invasive methods.

In recent years, the Tübingen Palatal Plate (TPP) has emerged as one of the primary non-invasive treatment options. TPP stabilizes the tongue position, helping to eliminate airway obstruction. Additionally, by relieving and advancing the tongue, it stimulates mandibular growth and significantly improves feeding in newborns, reducing the need for surgical interventions such as tracheostomy.

This method is now available at specialized centers in the Czech Republic, including the Pediatric Department of the 2nd Faculty of Medicine, Charles University and University Hospital Motol, in collaboration with the Dental Department of the 3rd Faculty of Medicine, Charles University and FN KV Prague, and with Prague Cleft Center at FN KV, and the Facial Cleft Treatment Center in Brno.

A multidisciplinary team plays a vital role in the care of PRS patients, comprising pediatricians, ENT specialists, plastic and maxillofacial surgeons, orthodontists, and speech therapists. This team ensures treatment optimization and prevents complications.

This article focuses on the available treatment options for PRS in the Czech Republic, highlighting the benefits of TPP and new technologies, such as 3D printing, which allow for precisely tailored devices to enhance treatment efficacy.

Keywords: Pierre-Robin Sequence, Tübingen Palatal Plate, micrognathia, glossoptosis, cleft palate, airway obstruction, multidisciplinary approach

Accepted: April 10, 2025; Published: June 9, 2025  Show citation

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Novotný V, Koťová M, Doušová T, Obermannová B. Current management options of Pierre-Robin sequence. Ces-slov Pediat. 2025;80(3):148-153. doi: 10.55095/CSPediatrie2025/019.
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